Transfected cell immunoblot: extracts of COS cells transiently transfected with Myc-tagged Frataxin and untagged Kv2.1 plasmids and probed with N191/7 (left), 19E10 (middle) and N52A/42 (right) TC supe.
Anti-Frataxin Antibody
SKU: 75-207
Bulk Order Anti-Frataxin Antibody
Product Details
Frataxin
Frataxin is a highly conserved protein found in mitochondria. Frataxin is found many tissues including heart, spinal cord, liver, pancreas, dermal fibroblasts, peripheral blood lymphocytes and skeletal muscles. Frataxin functions as an iron chaperone involved in iron-sulfur biogenesis and heme biosynthesis and plays a role in iron homeostasis. Mutations in the Frataxin gene can result in Friederich ataxia.
Purified
1 mg/mL
Monoclonal
N191/7
IgG2b
ICC, WB
Mouse
FXN FRDA X25
25 kDa
Fusion protein amino acids 81-210 (C-terminus) of human Frataxin (also known as Fxn, Friedreich ataxia protein, FRDA and X25, accession number Q16595); Mouse: 92% identity (118/127 amino acids identical)
Human
AB_11001258
Store at ≤ -20 C for long term storage. For short term storage, store at 2-8 C. For maximum recovery of product, centrifuge the vial prior to removing the cap.